The Robin Anomalad: Micrognathia and Glossoptosis With Airway Obstruction
نویسنده
چکیده
When micrognathia (small jaw) and glossoptosis (falling backward of the tongue) occur in the newborn, there is a great danger of upper airway obstruction. These deformities are frequently associated with an incomplete cleft of the palate, and the entity has been referred to as the Pierre Robin syndrome. Robin was far from the first to recognize the anatomical condition that bears his name, but he does deserve credit for calling attention to the clinical significance of this problem. He pointed out that in severe cases death was inevitable. In spite of his publications, it has taken many years for this knowledge to become widespread, and for an effective method of treatment to be developed (Robin, 1923a, 1927b, 1928, 1934).
منابع مشابه
Case report of Pierre Robin sequence with severe upper airway obstruction who was rescued by fiberoptic nasotracheal intubation
BACKGROUND Pierre Robin sequence (PRS) refers to the association of micrognathia, glossoptosis, and airway obstruction. Cases with severe dyspnea due to upper airway obstruction immediately after birth are very rare. We here report two cases with PRS who developed severe dyspnea due to morphological abnormality immediately after birth and were rescued by fiberoptic nasotracheal intubation. CA...
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